Ubiquitin-Specific Peptidase 37: The Master Orchestrator of Cancer Cells

How a cellular regulator becomes a catalyst for cancer development and therapy resistance

Molecular Biology Cancer Research Therapeutic Targets

The Unseen Conductor of Cellular Chaos

Imagine a world where the recycling system in a city suddenly starts working in reverse—instead of breaking down garbage, it carefully retrieves discarded items from trash heaps and returns them to homes and businesses. Soon, the city would become overwhelmed with accumulated junk, systems would fail, and chaos would ensue. This is precisely what happens in our cells when a specialized enzyme called Ubiquitin-Specific Peptidase 37 (USP37) goes rogue in cancer cells.

Key Insight

USP37 functions as a master regulator of protein stability within our cells, determining which proteins should be preserved and which should be discarded.

When this regulation is disrupted, normally short-lived proteins that should be rapidly removed instead accumulate to dangerous levels, driving uncontrolled cell growth and cancer development 1 . Recent research has illuminated USP37's critical role as a catalyst for some of the most aggressive forms of cancer, making it a promising target for next-generation cancer therapies. In this article, we'll explore how this cellular conductor can sometimes direct a symphony of chaos, and how scientists are learning to silence its baton.

The Ubiquitin System: Cellular Housekeeping and Its Saboteur

To understand USP37's role in cancer, we must first appreciate the elegant recycling system within our cells—the ubiquitin-proteasome pathway. This system acts as the cell's quality control and waste management service, ensuring that proteins are present in the right quantities at the right times.

The Ubiquitin-Proteasome Pathway

1
Ubiquitin Activation

A small protein called ubiquitin is first activated by an E1 enzyme in an energy-consuming process 1 .

2
Ubiquitin Conjugation

The activated ubiquitin is transferred to an E2 enzyme 1 3 .

3
Protein Tagging

An E3 enzyme facilitates transfer of ubiquitin from E2 to specific target proteins, marking them for destruction 1 3 .

4
Protein Degradation

Polyubiquitinated proteins are recognized and broken down by the proteasome—the cell's recycling center 1 .

This ubiquitin code creates a sophisticated language that controls not only protein destruction but also protein activity, location, and interactions 1 . Deubiquitinating enzymes (DUBs) like USP37 serve as the editors of this language, removing ubiquitin tags and thereby rescuing proteins from destruction 1 6 . While this editing function is essential for normal cellular operations, when USP37 becomes overactive in cancer cells, it saves proteins that should be destroyed, allowing them to accumulate and drive malignant transformation.

USP37: The Molecular Mastermind in Cancer Development

USP37 belongs to the largest family of deubiquitinating enzymes, known as ubiquitin-specific proteases (USPs), which account for approximately 60% of all human DUBs 9 . Under normal conditions, USP37 plays carefully regulated roles in cell division and DNA replication. However, in cancer cells, USP37 is frequently overexpressed or dysregulated, transforming it from a cellular custodian into a cancer-causing accomplice.

Cell Cycle Manipulation

USP37 directly controls the G1/S transition—a critical checkpoint determining when a cell commits to division 1 .

Oncogene Stabilization

USP37 stabilizes several powerful cancer-driving proteins (oncogenes), including c-Myc, a transcription factor that promotes cell growth and proliferation 6 .

Metastasis Promotion

USP37 enhances cancer metastasis—the process by which cancer cells spread to distant organs 1 .

Key Cancer-Promoting Proteins Stabilized by USP37

Target Protein Function in Cancer Cancer Types Where Identified
Cyclin A Drives cell cycle progression Multiple cancers
c-Myc Promotes cell growth and proliferation Lung cancer
SNAI1 Triggers epithelial-mesenchymal transition Breast cancer
14-3-3γ Activates MAPK signaling pathway Breast and lung cancers
HIF2α Promotes adaptation to low oxygen Kidney cancer

A Crucial Experiment: Demonstrating USP37's Cancer-Driving Capabilities

While observational studies had noted USP37 overexpression in various cancers, a pivotal experiment provided direct evidence of its transformative potential. Researchers designed a comprehensive approach to test whether USP37 could directly contribute to tumor formation and progression.

Methodology: Step-by-Step Experimental Design

Cell Line Selection

Researchers selected Ba/F3 cells (a murine pro-B cell line) and human cancer cell lines (H1299 lung cancer and MCF7 breast cancer cells) for their experiments 3 .

USP37 Manipulation

They introduced additional USP37 genes into Ba/F3 cells to overexpress the enzyme and used RNA interference techniques to reduce USP37 levels in cancer cell lines 3 .

Animal Tumor Model

Ba/F3 cells overexpressing USP37 were subcutaneously transplanted into the flanks of NOD/SCID mice, with a control group receiving mock-transfected cells with normal USP37 levels 3 .

Tumor Monitoring

Tumor growth was tracked for 6 weeks, with regular measurements of tumor size and volume 3 .

Cell-Based Assays

Migration assays were performed by creating "wounds" in cell monolayers and measuring closure time; proliferation rates were assessed in cells with altered USP37 expression 3 .

Results and Analysis: Compelling Evidence of USP37's Role

Tumor Formation in Mouse Model
USP37 Group
100% tumor incidence
Control Group
0% tumor incidence

The experimental results provided unambiguous evidence of USP37's cancer-promoting functions:

  • In Vivo Tumor Formation: Mice transplanted with USP37-overexpressing Ba/F3 cells developed substantial tumors that grew rapidly over the 6-week study period 3 .
  • Histological Analysis: Examination revealed high cellularity with spindle cells and atypical nuclei, suggesting aggressive fibrosarcoma 3 .
  • Cell Migration and Proliferation: USP37 overexpression significantly accelerated wound closure, while knocking down USP37 delayed wound closure and reduced proliferation 3 .

Scientific Significance

This crucial experiment demonstrated that USP37 isn't merely correlated with cancer but actively drives tumor formation and progression. The stabilization of 14-3-3γ by USP37 emerged as a key mechanism in this process 3 . The 14-3-3γ protein normally participates in various signaling pathways, but when stabilized and accumulated due to USP37 activity, it activates the MAPK signaling cascade—a known driver of cell proliferation and survival in cancer 3 .

The implications of these findings are profound: they suggest that inhibiting USP37 could potentially reverse these cancer-promoting effects, providing a rationale for developing USP37-targeted therapies.

Therapeutic Implications: Turning the Enemy into an Ally

The discovery of USP37's multifaceted role in cancer progression has positioned it as an attractive therapeutic target. Several promising approaches are emerging:

USP37 Inhibition Strategies

Researchers are actively developing small molecule inhibitors that can specifically block USP37's deubiquitinating activity 9 .

Combination Therapies

USP37 inhibitors show particular promise when combined with conventional chemotherapy 8 9 .

Targeting Cancer Stem Cells

USP37 is highly expressed in breast cancer stem cells (BCSCs)—cells responsible for tumor initiation and therapy resistance 8 .

USP37's Role in Therapy Response Across Cancer Types

Cancer Type Effect of USP37 Expression Potential Therapeutic Approach
Breast Cancer Confers resistance to cisplatin USP37 inhibition + chemotherapy
Lung Cancer Stabilizes c-Myc, driving proliferation USP37 inhibitors alone or in combination
Multiple Cancers Promotes cancer stem cell characteristics USP37-targeted therapies to prevent recurrence

The Scientist's Toolkit: Essential Research Reagents

Studying a complex enzyme like USP37 requires specialized research tools and reagents. Below are key components of the experimental toolkit that scientists use to unravel USP37's functions:

Reagent/Technique Primary Function Application in USP37 Research
Co-immunoprecipitation (Co-IP) Identifies protein-protein interactions Confirmed USP37 binding to 14-3-3γ and other partners 3
RNA Interference Reduces specific gene expression Knocking down USP37 to study functional consequences 3
Glutathione S-Transferase Pull-Down Assays Tests direct protein interactions Validated direct binding between USP37 and its targets 3
Ubiquitination Assays Measures protein ubiquitination status Demonstrated USP37-mediated deubiquitination of substrates 3
Cell Cycle Synchronization Agents Halts cells at specific cycle stages Revealed cell cycle-dependent fluctuation of USP37 1
NOD/SCID Mice Immunodeficient animal model Tested tumor-forming ability of USP37-expressing cells 3

Conclusion: From Molecular Understanding to Clinical Hope

The journey to understand Ubiquitin-Specific Peptidase 37 exemplifies how basic scientific research can reveal unexpected insights into human disease. What began as fundamental investigations into protein degradation mechanisms has uncovered a key player in cancer development and progression. USP37 sits at the nexus of multiple cancer-promoting pathways, making it a compelling therapeutic target for future cancer treatments.

Open Questions

Researchers are still working to identify all of USP37's protein substrates and regulatory mechanisms.

Current Research

The development of specific, potent USP37 inhibitors represents an active area of pharmaceutical research.

As research advances, the hope is that USP37-targeted therapies will join the anticancer arsenal, potentially providing new options for patients with aggressive, treatment-resistant cancers. By understanding and targeting the very mechanisms that cancer cells use to survive and thrive, we move closer to effective strategies for combating this complex disease.

References